Immunoglobulin Deficiencies: The B-Lymphocyte Side of DiGeorge Syndrome
نویسندگان
چکیده
منابع مشابه
Immunoglobulin deficiencies: the B-lymphocyte side of DiGeorge Syndrome.
DiGeorge syndrome is associated with a T-lymphocyte immunodeficiency. The prevalence of hypogammaglobulinemia has not been reported. We found that 3% of patients with DiGeorge syndrome were receiving immunoglobulin replacement therapy and 6% of patients over the age of 3 years had hypogammaglobulinemia. We conclude that DiGeorge syndrome is associated with significant humoral immune deficiency.
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ژورنال
عنوان ژورنال: PEDIATRICS
سال: 2013
ISSN: 0031-4005,1098-4275
DOI: 10.1542/peds.2013-2294ffff